From: Chitotriosidase - a putative biomarker for sporadic amyotrophic lateral sclerosis
 | CSF for iTRAQ study | CSF for validation | ||
---|---|---|---|---|
Gender | Male – 7 (70%) | Female – 3 (30%) | Male – 10 (62.5%) | Female – 6 (37.5%) |
Age at presentation (Mean ± SD) | 47.40 ± 4.95 (38 – 54) Years | 47.38 ± 5.38 (38 – 54) Years | ||
Age at onset | 46 ± 5.05 (37 – 53) Years | 46.28 ± 5.36 (37 – 53) Years | ||
Duration of illness (Mean ± SD) | 15.9 ± 13.4 (4.0 – 48) months | 14.19 ± 10.59 (4.0 – 48) months | ||
Onset Patter: Bulbar | 1 (10%) | 5 (31.25%) | ||
Limb onset | 9 (90%) | 11 (68.75%) | ||
Upper Limbs | 9 | 11 | ||
Lower Limbs | 6 | 7 | ||
Speech affected | 80% (Mild – 30%, Moderate – 30%, Severe – 20%) | 87.5% (Mild – 31.25%, Moderate – 31.25%, Severe – 25%) | ||
Dysphagia | 80% (Mild – 30%, Moderate – 30%, Severe – 20%) | 93.75% (Mild – 31.25%, Moderate – 18.75%, Severe -12.5%) | ||
Spasticity | 9 cases, with evidence of pyramidal signs in the form of spasticity and exaggerated Deep Tendon Reflexes | 11 cases, with evidence of pyramidal signs in the form of spasticity and exaggerated Deep Tendon Reflexes |